Management of an esophagogastric fibromatosis in a child: A case report

Koyluoglu G., Yildiz E., Koyuncu A., Atalar M.

JOURNAL OF PEDIATRIC SURGERY, cilt.39, sa.4, ss.640-642, 2004 (SCI İndekslerine Giren Dergi) identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 39 Konu: 4
  • Basım Tarihi: 2004
  • Doi Numarası: 10.1016/j.jpedsurg.2003.12.025
  • Sayfa Sayıları: ss.640-642


Intraabdominal fibromatosis is an uncommon neoplasm. The aggressive nature of these tumors and the potential for major morbidity secondary to resection can present a difficult surgical dilemma. A 9-year-old boy presented with anemia and vomiting. He had esophagogastric fibromatosis diagnosed and underwent distal esophagectomy, total gastrectomy, Hunt-Lawrence jejunal pouch, and Roux-en-Y esophagojejunostomy. This report describes the successful surgical management of an esophagogastric fibromatosis for the first time in the English-language literature. The management of this tumor is discussed with particular regard to the very unusual clinical presentation.